🔹 Introduction:

👉🏻 The affected teeth (both dentitions) are grey to yellow brown with broad crowns and constriction at cervical area resulting in tulip shape.

👉🏻 The enamel is easily broken, exposure of dentin ➡️ accelerated attrition.

👉🏻 Normal non-mineralized pulp chambers and canals

👉🏻 This condition is inherited in an autosomal dominant pattern, as a result of mutations on chromosome 4q21, in the dentine sialophosphoprotein gene (DSPP).

🔹Classification:

🔹Radiographic Features:

🔹Histopathological Features:

👉🏻 Mesodermal disturbance.

👉🏻 Dentin composed of irregular tubules with large areas of unclassified matrix. The tubules are larger in diameter & less numerous.

👉🏻 Odontoblasts – dentinal matrix not layed properly & they are entrapped within this matrix.

CHEMICAL FEATURES:
• Increased water content (60 times the normal)
• Decreased inorganic content

🔹Treatment: Cast Metal crowns & Jacket crowns

Dr. Mehnaz Memon🖊

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References:

1. Shafer’sTextbook Of Oral Pathology (7th Ed)
2. Image Source: International Journal of Medicine Research; Dr G’s Toothpix; Google