DENTINOGENESIS IMPERFECTA 

  1. Not associated with osteogenesis imperfecta 
  2. Mutation in gene – DSPP – dentin sialo phospho protein 
  3. DSPP located on chromosome number 4 
  4. Revised shield classification
    1. Common traits seen in both types
      1. Flat DEJ line 
      2. Gene = DSSP

Type 1
Opalescent dentin type 
Type 2
Brandy white type 

Bulbous crowns are seen With cervical constriction Giving tulip shaped crownsWHY? Because of atypical dentin formation = obliteration of pulp chambers

Large sized pulp chambers Very thin dentin – hence, radiographically SHELL TEETH 

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